A Remarkable Orbital Apex Mass in a Young Man

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Identifier walsh_1986_s6_c4
Title A Remarkable Orbital Apex Mass in a Young Man
Creator Alfredo A. Sadun, MD, PhD, Flora L. Thornton Chair, Professor of Ophthalmology and Neurological Surgery, Keck School of Medicine at USC
Subject Tolosa-Hunt Syndrome; Granular Cell Tumor; Papilledema; Neurilemmoma; Exophthalmos
History A 29-year old male with stiff neck and intermittent diplopia.
Pathology Cellular mass composed of oval, spindle-shaped polyhedral cells containing acidophilic cytoplasm consistent with malignant granular cell myoblastoma.
Disease/Diagnosis Malignant granular cell myoblastoma
Clinical VA: 20/20 OU
Presenting Symptom Stiff neck, Diplopia
Neuroimaging CT
Treatment Corticosteroids; Surgery; XRT
Date 1986-02-20
References 1. Al-Sarraf M, Lo'Jd AV, Vaitkevioius KV: Malignant granular cell tumor. Arch. Pathol. 91:550-553, 1971. 2. Adaracio SR, Lumsden CE: Light and electron microscopic studies on the granular cell myoblastoma of the tongue. J. Pathol. 97:339-55, 1969. 3. Armin A, Connelly EM, Rowden G: An immunoperoxidase investigation of S-100 protein in granular cell myoblastomas: evidence for Schwann cell derivation. Am. J. Clin. Pathol. 79:37-44, 1983. 4.Azzopardi JG: Histogenesis of the granular cell "myoblastoma." J. Pathol. Bact. 71:85-94, 1956. 5. Bunt AH and Bensinger, RE. Alveolar soft-part sarcoma of the orbit. Ophthalmology 88:1339-1346, 1981. 6. Fishe ER, Wechsler H: Granular cell myoblastoma - misnomer. Cancer 15:936-954, 1962. 7. Garancis JC, Komorowski RA, Kuzma JF: Granular cell myoblastoma. Cancer 25:542-550, 1970. 8. Nakazato Y, Ishizeki J, Takahashi K, Yamaguchi H: Immunohisto-chemical localization of S-100 protein in granular cell myoblastoma. Cancer 49:1624-1628, 1982. 9. Ravich A, Stout AP, and Ravich RA: Malignant granular cell myoblastoma involving the urinary bladder. Ann. Surg. 121:361-372, 1945. 10. Sobel HJ, Schwarz R, Marquet E: Light and electron-microscope study of the origin of granular-cell myoblastoma. J. Pathol. 109: 101-111, 1973. 11. Sobel HJ, Marquet E and Schwartz R: Is schwannoma related to granular cell myoblastoma? Arch. Pathol. 95:396-401, 1973. 12. Stefansson K, Wollmann RL: S-100 protein in granular cell tumors (granular cell myoblastomas). Cancer 49:1834-1838, 1982. 13. Von Bahr G: A case of myoblastic myoma of the lacrimal sac. Acta Ophthalmol. 16:109, 1938.
Language eng
Format application/pdf
Type Text
Source 18th Annual Frank Walsh Society Meeting
Relation is Part of Case 4, Session 6, Walsh Session, NANOS 1986
Collection Neuro-ophthalmology Virtual Education Library: NOVEL http://NOVEL.utah.edu
Publisher Spencer S. Eccles Health Sciences Library, University of Utah
Holding Institution North American Neuro-Ophthalmology Association. NANOS Executive Office 5841 Cedar Lake Road, Suite 204, Minneapolis, MN 55416
Rights Management Copyright 2008. For further information regarding the rights to this collection, please visit: https://NOVEL.utah.edu/about/copyright
ARK ark:/87278/s61r6t86
Contributor Primary Sadun, Alfredo A.
Contributor Secondary Borchert, Mark S.; Feldon, Steven E.
Setname ehsl_novel_fbw
ID 178159
Reference URL https://collections.lib.utah.edu/ark:/87278/s61r6t86